Episodio – Síndrome de Marfan: fibrilina-1, microfibrillas y muerte por disección aórtica | USMLE Step 1 episode artwork

EPISODE · Feb 6, 2026 · 7 MIN

Episodio – Síndrome de Marfan: fibrilina-1, microfibrillas y muerte por disección aórtica | USMLE Step 1

from USMLE DREAMERS · host USMLE DREAMERS

Varón joven con dolor torácico y abdominal súbito, colapso hemodinámico y hemorragia interna fatal. Se analiza el papel de la fibrilina-1 en la matriz extracelular, la fisiopatología del síndrome de Marfan y la causa cardiovascular típica de muerte: dilatación, disección y ruptura aórtica.#USMLE #Step1 #USMLEDreamers #Genética #TejidoConectivo #Marfan #Aorta

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Episodio – Síndrome de Marfan: fibrilina-1, microfibrillas y muerte por disección aórtica | USMLE Step 1

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